13 October 2020>: Original Paper
Pediatric Liver Transplantation for Alagille Syndrome: Anesthetic Evaluation and Perioperative Management
Wen-He Yang 1ABF* , Liang Zhang 1ABCDEF* , Fu-Shan Xue 1ADG* , Azmat Riaz 2EF , Zhi-Jun Zhu 345ADG*DOI: 10.12659/AOT.924282
Ann Transplant 2020; 25:e924282
Table 1 Baseline patient and liver graft characteristics.
Case | Age (mo) | Gender | Weight (kg) | Height (cm) | Z Score# | Genetic type | CTP Score | PELD Score | Echocardiogram Abnormities | NYHA Classification |
---|---|---|---|---|---|---|---|---|---|---|
1 | 12 | Female | 7.5 | 66 | −3.60 | JAG1 | 8 | 12 | PFO, PAS | I |
2 | 27.5 | Male | 10.5 | 82 | −2.68 | * | 6 | 8 | Normal | I |
3 | 12 | Male | 9 | 82 | 1.96 | JAG1 | 8 | 13 | VSD, PDA | I |
4 | 149 | Male | 35.8 | 143 | −1.03 | JAG1 | 6 | 13 | PS | I |
5 | 16.5 | Male | 8.4 | 76 | −1.31 | JAG1 | 9 | 18 | Normal | I |
6 | 73 | Male | 15 | 102 | −3.49 | JAG1 | 5 | −3 | VSD | II |
7 | 65.5 | Male | 15 | 97 | −4.12 | JAG1 | 12 | 31 | PS | II |
8 | 23.5 | Female | 8.5 | 80 | −2.25 | * | 9 | 21 | BAVS | II |
9 | 17 | Male | 7.9 | 71.5 | −2.96 | JAG1 | 8 | 12 | PFO | I |
10 | 12 | Female | 6.3 | 68 | −2.80 | JAG1 | 7 | 10 | PS | I |
11 | 114 | Male | 17 | 122 | −2.69 | JAG1 | 5 | 3 | PS | I |
1 | Deceased | Whole | 321 | 4.28 | 5 | 710 | ||||
2 | Living related | Left lateral lobe | 226 | 2.15 | 2 | 83 | ||||
3 | Living related | Left lateral lobe | 267 | 2.97 | 2 | 117 | ||||
4 | Deceased, split | Left lobe with MHV | 525 | 1.47 | 3 | 570 | ||||
5 | Deceased, reduced-size | Left lateral lobe | 264 | 3.14 | 3 | 640 | ||||
6 | Living related | Left lateral lobe | 317 | 2.11 | 4 | 147 | ||||
7 | Living related | Left lobe with MHV | 306 | 2.04 | 2 | 150 | ||||
8 | Living related | Left lateral lobe | 214 | 2.52 | 2 | 90 | ||||
9 | Living related | Left lateral lobe | 253 | 3.20 | 2 | 79 | ||||
10 | Living related | Left lateral lobe | 200 | 3.18 | 1 | 67 | ||||
11 | Living related | Left lateral lobe | 272 | 1.60 | 2 | 100 | ||||
* Diagnosis based on clinical diagnostic criteria. # Height for age Z score (Data form Chinese Center for Disease Control and Prevention). BAVS – bicuspid aortic valve stenosis; CIT – cold ischemia time; CTP – Child-Turcotte-Pugh; GRWR – graft-to-recipient weight ratio; MHV – middle hepatic vein; PAS – pulmonary artery sling; PDA – patent ductas arteriosus; PELD – Pediatric End-stage Liver Disease; PFO – patent foramen ovale; PS – pulmonary stenosis; VSD – ventricular septal defect; WIT - warm ischemia time. |